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Preemptive rituximab prevents long-term relapses in immune-mediated thrombotic thrombocytopenic purpura.   Jestin M, Benhamou Y, Schelpe AS, Roose E, Provôt F, Galicier L, Hié  M,  Presne C, Poullin P, Wynckel A, Saheb S, Deligny C, Servais A,  Girault  S, Delmas Y, Kanouni T, Lautrette A, Chauveau D, Mousson C,  Perez P,  Halimi JM, Charvet-Rumpler A, Hamidou M, Cathébras P,  Vanhoorelbeke K,  Veyradier A, Coppo P; French Thrombotic  Microangiopathies Reference  Center. Blood 2018;132:2143-53.
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 An open conformation of ADAMTS-13 is a hallmark of acute acquired TTP.   Roose E, Schelpe AS, Joly BS, Peetermans M, Verhamme P, Voorberg J,   Greinacher A, Deckmyn H, De Meyer SF, Coppo P, Veyradier A,   Vanhoorelbeke K. J Thromb Haemost. 2018;16:378-88.